Calcinosis cutis is an uncommon entity defined as the deposition of amorphous calcium and phosphate salts under epidermis. Idiopathic calcinosis cutis occurs in the absence of any metabolic disorder or tissue damage. A 40-year-old multiparous female presented with vulvar nodular masses with discomfort during intercourse only. Physical examination revealed a yellowish colored non-tender, pedunculated nodules measuring approximately 3×1 cm in the left side of vulva. The mass localized between labia minora and labia majora was solid, surfaced with the white pigmentation, irregular, fixed and in sessile nature. Laboratory evaluation revealed normal serum calcium and phosphorus levels and all other laboratory values were within normal reference ranges. Total surgical excision of the mass was performed under general anesthesia.
The histopathological diagnosis revealed a calcinosis cutis of the vulva and no recurrence was detected 12 months after the initial treatment.